Herpes Zoster Oticus

(Geniculate Herpes; Ramsay Hunt Syndrome)

ByMickie Hamiter, MD, New York Presbyterian Columbia
Reviewed/Revised May 2023
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Herpes zoster oticus is an uncommon manifestation of herpes zoster that affects the 8th cranial nerve ganglia and the geniculate ganglion of the 7th (facial) cranial nerve.

Herpes zoster (shingles) is reactivation of varicella-zoster virus infection. Risk factors for reactivation include immunodeficiency secondary to cancer, chemotherapy, radiation therapy, and HIV infection. Typically, the virus remains latent in a dorsal root ganglion, and reactivation manifests as painful skin lesions in a dermatomal distribution. However, the virus rarely remains latent in the geniculate ganglion; when reactivated, the virus causes symptoms involving the 7th and 8th cranial nerves.

Symptoms and Signs of Herpes Zoster Oticus

Symptoms of herpes zoster oticus include

  • Severe ear pain with vesicles in the ear

  • Transient or permanent facial paralysis (resembling Bell palsy)

  • Vertigo lasting days to weeks

  • Hearing loss (which may be permanent or which may resolve partially or completely)

Vesicles occur on the pinna and in the external auditory canal along the distribution of the sensory branch of the facial nerve. Symptoms of meningoencephalitis (eg, headache, confusion, stiff neck) are uncommon. Sometimes other cranial nerves are involved.

Diagnosis of Herpes Zoster Oticus

  • Clinical evaluation

Diagnosis of herpes zoster oticus is usually clinical. If there is any question about viral etiology, vesicular scrapings may be collected for direct immunofluorescence or for viral cultures, and MRI is done to exclude other diagnoses.

Treatment of Herpes Zoster Oticus

  • Antivirals and corticosteroids

  • Sometimes for complete facial paralysis, surgical decompression of the fallopian canal

The role of surgical treatment of facial paralysis remains controversial; however, surgical decompression of the fallopian canal may be considered if the facial palsy is complete (no visible facial movement). Decompression must be done within 2 weeks of onset of the facial paralysis to be effective. Before surgery, electroneurography is done. Patients with a > 90% decrement in facial movement are usually candidates for decompression.

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